Case report
Persistent pulmonary hypertension of the newborn associated with
pulmonary atresia and intact interventricular septum
M Codispotia, J E Burnsa, S G Haworthb, D Simpsona, P S Mankada
a Department of
Cardiac Surgery, Royal Hospital for Sick Children, Sciennes Road,
Edinburgh EH9 1LF, UK, b Division of
Developmental Cardiology, Institute of Child Health, Hospital for Sick
Children, Great Ormond Street, London WC1N 3JH, UK
Correspondence to: Mr Mankad. email: pankaj.mankad{at}ed.ac.uk
Accepted for publication 29 June 1999
Neonates with pulmonary atresia and intact interventricular
septum (PAIVS) do not have pulmonary vascular disease secondary to
their heart abnormality. Persistent pulmonary hypertension of the
newborn has not been described in association with this condition. The
case is reported of a female neonate born with PAIVS, who
preoperatively had no clinical evidence or any risk factors for
persistent pulmonary hypertension of the newborn, but whose
postoperative course was highly suggestive of persistent pulmonary
hypertension; necropsy confirmed the features of pulmonary vascular disease.
Keywords: persistent pulmonary hypertension; pulmonary atresia and intact ventricular septum; pulmonary vascular disease; surgery; congenital heart defects
© 1999 by Heart
eLetters:
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- A 'Persistent' Problem with Pulmonary Atresia and Intact Ventricular Septum
- Pradeep Vaideeswar
- Online, 7 Jul 2000 [Full text]
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