Editorial
Clinical relevance of right ventricular dysplasia/cardiomyopathy
| The first 150 words of the full text of this article appear below. |
(Arrhythmogenic) right ventricular dysplasia, also called (arrhythmogenic) right ventricular cardiomyopathy (RVD/C) is a recently defined heart muscle disease of unknown origin that predominantly, although not exclusively, affects the right ventricular myocardium.
Its pathological hallmark is the atrophy of myocytes with fatty or fibro-fatty infiltration of the right ventricle.1 The typical clinical picture is related to ventricular tachyarrhythmias with left bundle branch block morphology, which may cause sudden death,1 2 while a less frequent presentation is "right" heart failure. The disease may be localised or widespread, with biventricular involvement in some cases.3
In the past decade several investigators have contributed to the knowledge of this "new" cardiomyopathy4; nevertheless, there are still many uncertainties that deserve further studies. This editorial is mainly oriented to some still unsolved problems of RVD/C.
Aetiologic theoriesSeveral hypotheses have been advocated to explain the cause and
pathogenesis of RVD/C. The first, that explains the term
"dysplasia"
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This article has been cited by other articles:
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Kayser, H. W. M., van der Wall, E. E., Sivananthan, M. U., Plein, S., Bloomer, T. N., de Roos, A.
(2002). Diagnosis of Arrhythmogenic Right Ventricular Dysplasia: A Review. RadioGraphics
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