| HOME | HELP | FEEDBACK | SUBSCRIPTIONS | ARCHIVE | SEARCH | TABLE OF CONTENTS | REGISTER |
|
|
|
|
|||||||||||||
|
|
|||||||||||||||
Departments of Cardiology and Pathology, University of Padova,
Italy
Correspondence to: Domenico Corrado MD, Department of Cardiology, University of Padua Medical School, Via Giustiniani 2 - 35121 Padova, Italy email: cardpath@ux1.unipd.it
| The first 150 words of the full text of this article appear below. |
 |
Introduction |
|---|
Arrhythmogenic
right ventricular cardiomyopathy (ARVC) is a myocardial disease, often
familial, that is characterised pathologically by fibrofatty
replacement of the right ventricular myocardium, and clinically by
ventricular arrhythmias of right ventricular origin which may lead to
sudden death, mostly in young people and athletes.1-5 The
term "dysplasia" was originally used to describe an entity that was
considered to be the result of a developmental defect of the right
ventricular myocardium.1 A better understanding of
clinical manifestations as well as morphologic findings does not
support the theory of a congenital absence of the myocardium, but is in
keeping with a non-ischaemic, ongoing atrophy of the right ventricular
myocardium, most likely genetically determined, which becomes
symptomatic in adolescents and young adults.2-4 On the
basis of its nature of progressive heart muscle disease of unknown
aetiology, ARVC has been more appropriately included among the
cardiomyopathies in the recent classification proposed by the task
This article has been cited by other articles:
|
|
 |
|
  R. Nijveldt, A. M. Beek, T. Germans, O. Bondarenko, and A. C. van Rossum Arrhythmogenic right ventricular cardiomyopathy with evidence of biventricular involvement Can. Med. Assoc. J., June 19, 2007; 176(13): 1819 - 1821. [Full Text] [PDF]
|
|
|
|
 |
|
 P. Syrris, D. Ward, A. Asimaki, A. Evans, S. Sen-Chowdhry, S. E. Hughes, and W. J. McKenna Desmoglein-2 mutations in arrhythmogenic right ventricular cardiomyopathy: a genotype-phenotype characterization of familial disease Eur. Heart J., March 1, 2007; 28(5): 581 - 588. [Abstract] [Full Text] [PDF]
|
|
|
|
 |
|
 H. Tandri, E. Castillo, V. A. Ferrari, K. Nasir, D. Dalal, C. Bomma, H. Calkins, and D. A. Bluemke Magnetic Resonance Imaging of Arrhythmogenic Right Ventricular Dysplasia: Sensitivity, Specificity, and Observer Variability of Fat Detection Versus Functional Analysis of the Right Ventricle J. Am. Coll. Cardiol., December 5, 2006; 48(11): 2277 - 2284. [Abstract] [Full Text] [PDF]
|
|
|
|
 |
|
 R. Vitiello Commentary: the value of the ECG in the preparticipation sports physical examination: the Italian experience. Pediatr. Rev., November 1, 2006; 27(11): e75 - e76. [Full Text] [PDF]
|
|
|
|
|
|
D. Dalal, C. James, R. Devanagondi, C. Tichnell, A. Tucker, K. Prakasa, P. J. Spevak, D. A. Bluemke, T. Abraham, S. D. Russell, et al. Penetrance of Mutations in Plakophilin-2 Among Families With Arrhythmogenic Right Ventricular Dysplasia/Cardiomyopathy J. Am. Coll. Cardiol., October 3, 2006; 48(7): 1416 - 1424. [Abstract] [Full Text] [PDF]
|
|
|
|
 |
|
 C. Wren Screening children with a family history of sudden cardiac death. Heart, July 1, 2006; 92(7): 1001 - 1006. [Full Text] [PDF]
|
|
|
|
 |
|
 D. Dalal, L. H. Molin, J. Piccini, C. Tichnell, C. James, C. Bomma, K. Prakasa, J. A. Towbin, F. I. Marcus, P. J. Spevak, et al. Clinical Features of Arrhythmogenic Right Ventricular Dysplasia/Cardiomyopathy Associated With Mutations in Plakophilin-2 Circulation, April 4, 2006; 113(13): 1641 - 1649. [Abstract] [Full Text] [PDF]
|
|
|
|
|
|
P. Syrris, D. Ward, A. Asimaki, S. Sen-Chowdhry, H. Y. Ebrahim, A. Evans, N. Hitomi, M. Norman, A. Pantazis, A. L. Shaw, et al. Clinical Expression of Plakophilin-2 Mutations in Familial Arrhythmogenic Right Ventricular Cardiomyopathy Circulation, January 24, 2006; 113(3): 356 - 364. [Abstract] [Full Text] [PDF]
|
|
|
|
|
|
D. Dalal, K. Nasir, C. Bomma, K. Prakasa, H. Tandri, J. Piccini, A. Roguin, C. Tichnell, C. James, S. D. Russell, et al. Arrhythmogenic Right Ventricular Dysplasia: A United States Experience Circulation, December 20, 2005; 112(25): 3823 - 3832. [Abstract] [Full Text] [PDF]
|
|
|
|
|
|
A. Frustaci, S. G. Priori, M. Pieroni, C. Chimenti, C. Napolitano, I. Rivolta, T. Sanna, F. Bellocci, and M. A. Russo Cardiac Histological Substrate in Patients With Clinical Phenotype of Brugada Syndrome Circulation, December 13, 2005; 112(24): 3680 - 3687. [Abstract] [Full Text] [PDF]
|
|
|
|
 |
|
 M. Yoda, K. Minami, D. Fritzsche, G. Tendrich, S. Schulte-Eistrup, and R. Koerfer Three Cases of Orthotopic Heart Transplantation for Arrhythmogenic Right Ventricular Cardiomyopathy Ann. Thorac. Surg., December 1, 2005; 80(6): 2358 - 2360. [Abstract] [Full Text] [PDF]
|
|
|
|
|
|
H. L. Tan, N. Hofman, I. M. van Langen, A. C. van der Wal, and A. A.M. Wilde Sudden Unexplained Death: Heritability and Diagnostic Yield of Cardiological and Genetic Examination in Surviving Relatives Circulation, July 12, 2005; 112(2): 207 - 213. [Abstract] [Full Text] [PDF]
|
|
|
|
|
|
A. Verma, F. Kilicaslan, R. A. Schweikert, G. Tomassoni, A. Rossillo, N. F. Marrouche, V. Ozduran, O. M. Wazni, S. C. Elayi, L. C. Saenz, et al. Short- and Long-Term Success of Substrate-Based Mapping and Ablation of Ventricular Tachycardia in Arrhythmogenic Right Ventricular Dysplasia Circulation, June 21, 2005; 111(24): 3209 - 3216. [Abstract] [Full Text] [PDF]
|
|
|
|
|
|
D. Corrado, C. Basso, L. Leoni, B. Tokajuk, B. Bauce, G. Frigo, G. Tarantini, M. Napodano, P. Turrini, A. Ramondo, et al. Three-Dimensional Electroanatomic Voltage Mapping Increases Accuracy of Diagnosing Arrhythmogenic Right Ventricular Cardiomyopathy/Dysplasia Circulation, June 14, 2005; 111(23): 3042 - 3050. [Abstract] [Full Text] [PDF]
|
|
|
|
|
|
D. Corrado, A. Pelliccia, H. H. Bjornstad, L. Vanhees, A. Biffi, M. Borjesson, N. Panhuyzen-Goedkoop, A. Deligiannis, E. Solberg, D. Dugmore, et al. Cardiovascular pre-participation screening of young competitive athletes for prevention of sudden death: proposal for a common European protocol: Consensus Statement of the Study Group of Sport Cardiology of the Working Group of Cardiac Rehabilitation and Exercise Physiology and the Working Group of Myocardial and Pericardial Diseases of the European Society of Cardiology Eur. Heart J., March 1, 2005; 26(5): 516 - 524. [Abstract] [Full Text] [PDF]
|
|
|
|
|
|
J.-S. Hulot, X. Jouven, J.-P. Empana, R. Frank, and G. Fontaine Natural History and Risk Stratification of Arrhythmogenic Right Ventricular Dysplasia/Cardiomyopathy Circulation, October 5, 2004; 110(14): 1879 - 1884. [Abstract] [Full Text] [PDF]
|
|
|
|
|
|
C. Chimenti, M. Pieroni, A. Maseri, and A. Frustaci Histologic findings in patients with clinical and instrumental diagnosis of sporadic arrhythmogenic right ventricular dysplasia J. Am. Coll. Cardiol., June 16, 2004; 43(12): 2305 - 2313. [Abstract] [Full Text] [PDF]
|
|
|
|
|
|
D. Corrado, L. Leoni, M. S. Link, P. D. Bella, F. Gaita, A. Curnis, J. U. Salerno, D. Igidbashian, A. Raviele, M. Disertori, et al. Implantable Cardioverter-Defibrillator Therapy for Prevention of Sudden Death in Patients With Arrhythmogenic Right Ventricular Cardiomyopathy/Dysplasia Circulation, December 23, 2003; 108(25): 3084 - 3091. [Abstract] [Full Text] [PDF]
|
|
|
|
 |
|
 M. Scoote and A. J Williams The cardiac ryanodine receptor (calcium release channel): Emerging role in heart failure and arrhythmia pathogenesis Cardiovasc Res, December 1, 2002; 56(3): 359 - 372. [Abstract] [Full Text] [PDF]
|
|
|
|
|
|
C. Wren Sudden death in children and adolescents Heart, October 1, 2002; 88(4): 426 - 431. [Full Text] [PDF]
|
|
|
|
 |
|
 H. W. M. Kayser, E. E. van der Wall, M. U. Sivananthan, S. Plein, T. N. Bloomer, and A. de Roos Diagnosis of Arrhythmogenic Right Ventricular Dysplasia: A Review RadioGraphics, May 1, 2002; 22(3): 639 - 648. [Abstract] [Full Text] [PDF]
|
|
|
|
|
|
C. Gemayel, A. Pelliccia, and P. D. Thompson Arrhythmogenic right ventricular cardiomyopathy J. Am. Coll. Cardiol., December 1, 2001; 38(7): 1773 - 1781. [Abstract] [Full Text] [PDF]
|
|
|
|
|
|
C G De Pasquale and W F Heddle Left sided arrhythmogenic ventricular dysplasia in siblings Heart, August 1, 2001; 86(2): 128 - 130. [Abstract] [Full Text] [PDF]
|
|
|
|
|
|
D. Corrado, C. Basso, and G. Thiene Sudden cardiac death in young people with apparently normal heart Cardiovasc Res, May 1, 2001; 50(2): 399 - 408. [Abstract] [Full Text] [PDF]
|
|
|
|
 |
|
 H. Calkins Premature Ventricular Depolarizations during Exercise N. Engl. J. Med., September 21, 2000; 343(12): 879 - 880. [Full Text]
|
|
| HOME | HELP | FEEDBACK | SUBSCRIPTIONS | ARCHIVE | SEARCH | TABLE OF CONTENTS | REGISTER |
