Table 1

Patient characteristics

PatientsHealthy controls
NYHA, New York Heart Association functional class; RV, right ventricular.
Male/female (n)19/1819/18
Age at study (years)16.8 (9), range 6–3317.2 (9), range 6–33
    Children (age <18 years) (n=24)12 (3)12 (3)
    Adults (n=13)29 (7)28 (9)
Body surface area (m2)1.7 (0.49)1.7 (0.42)
Age at operative repair (years)4.5 (3)
Time of follow up (years)14 (7)
Right ventriculotomy (n)10
Transannular patch (n)13
Restrictive RV filling pattern (n)13
Pulmonary stenosis (>30 mm Hg) (n)3
Pulmonary regurgitation (n)34
Functional state at time of study
    NYHA class I (n)34
    NYHA class II (n)3