List of conditions considered to be complex with special risks and complications
| Usual name | Common synonyms/categories |
|---|---|
| *Surgery can be difficult in adults. Intervention requires specialist experience. | |
| Absent left and right atrioventricular connection | Mitral atresia, tricuspid atresia |
| Anomalous pulmonary venous connection (total or partial) | |
| Aortic valve or aortic root disease requiring intervention in childhood or adolescence | Congenital aortic stenosis or regurgitation, aorto-left ventricular fistula, sinus of Valsalva fistula or aneurysm |
| Atrioventricular septal defects (partial and complete) | Primum ASD, atrioventricular canal, endocardial cushion defects |
| Coarctation of aorta | |
| Common arterial trunk | Truncus arteriosus, hemitruncus |
| Common atrium | Single atrium. Often associated with laevocardia, anomalies of systemic veins |
| Transposition of great arteries | d-transposition, TGA, VA discordance |
| Congenitally corrected transposition | L-transposition, AV and VA discordance) |
| Congenital coronary artery anomalies, fistulae (unless incidental finding) | |
| Cor triatriatum, left and right sided | Divided atrium |
| Cyanotic congenital heart disease—all types | |
| Double outlet left ventricle | |
| Double outlet right ventricle | Taussig-Bing anomaly |
| Ebstein’s malformation | |
| Hypoplastic left ventricle | |
| Hypoplastic right ventricle | Pulmonary atresia with intact ventricular septum |
| Infundibular stenosis | Right ventricular outflow obstruction |
| Mitral valvar anomaly (congenital) | Parachute mitral valve, clefts, absent leaflet, Shone’s syndrome |
| Functionally single ventricle | Single ventricle (double inlet ventricle, common ventricle) |
| Persistent ductus arteriosus* | |
| Pulmonary atresia with ventricular septal defect | Pulmonary atresia with congenital systemic collaterals. Tetralogy of Fallot with pulmonary atresia |
| Pulmonary hypertension complicating congenital heart disease | Eisenmenger’s syndrome, and residual postoperative pulmonary hypertension after defect or duct closure |
| Pulmonary valvar regurgitation or stenosis (moderate or greater), including absent pulmonary valve | |
| Subvalvar or supravalvar aortic stenosis | |
| Tetralogy of Fallot | |
| Valved conduits | Usually right sided—homografts, dura, fascia, Carpentier Edwards, valveless, pericardial |
| Ventricular septal defect (complex) | Includes ventricular septal defects with aortic regurgitation, absent leaflets, coarctation, mitral valve disease, straddling tricuspid or mitral valve, subaortic stenosis, two chambered right ventricle |
| Other anomalies of atrioventricular connection, for example, criss-cross heart, upstairs-downstairs heart | |
| Heterotaxy syndromes | Isomerism of atrial appendages, right or left |