Table 1

Muscular manifestations of myotonic dystrophy (DM1)

Myotonia▸ Active and evoked
Muscular dystrophy and wasting▸ Facial and masticatory muscles (facies myotonica)
▸ Axial compartment
▸ Semidistal compartment
▸ Distal compartment
▸ Pharyngeal muscles (nasal speech, dysphagia )
▸ Respiratory muscles
Central nervous system▸ Cognitive impairment
▸ Mental retardation
▸ Attentive disorders