Diseases of the respiratory system associated with pulmonary hypertension (except primary pulmonary hypertension, pulmonary thromboembolic disease, and diseases of the pulmonary vascular bed)
| *Very frequent cause of pulmonary hypertension. |
| †Relatively frequent cause of pulmonary hypertension. |
| Obstructive lung diseases |
| ▸ COPD* (chronic obstructive bronchitis, emphysema and their association) |
| ▸ Asthma (with irreversible airway obstruction) |
| ▸ Cystic fibrosis† |
| ▸ Bronchiectasis |
| ▸ Bronchiolitis obliterans |
| Restrictive lung diseases |
| ▸ Neuromuscular diseases: amyotrophic lateral sclerosis, myopathy, bilateral diaphragmatic paralysis, etc |
| ▸ Kyphoscoliosis† |
| ▸ Thoracoplasty |
| ▸ Sequelae of pulmonary tuberculosis |
| ▸ Sarcoidosis |
| ▸ Pneumoconiosis† |
| ▸ Drug related lung diseases |
| ▸ Extrinsic allergic alveolitis |
| ▸ Connective tissue diseases |
| ▸ Idiopathic interstitial pulmonary fibrosis† |
| ▸ Interstitial pulmonary fibrosis of known origin |
| Respiratory insufficiency of “central” origin |
| ▸ Central alveolar hypoventilation |
| ▸ Obesity–hypoventilation syndrome† (formerly “Pickwickian syndrome”) |
| ▸ Sleep apnoea syndrome† |