Initial mean characteristics of the MD patients without a pacemaker
| Group 1 (n=70) mean±SD | Group 2 (n=45) mean±SD | Group 3 (n=25) mean±SD | |
| Age (years) | 40±15 | 41.5±15 | 37.2±14 |
| Women n, (%) | 28 (40) | 21 (46) | 7 (28) |
| Brooke score | 3.3±2.3 | 3.4±2.6 | 3.4±1.7 |
| Abnormal ECG | 20 (28.5) | 14 (31.1) | 8 (32) |
| Spontaneous AF, n (%) | 8 (11) | 6 (13.3) | 2 (8) |
| Spontaneous NSVT, n | 1 | 1 | 0 |
| LVEF (%) | 59.4±10 | 57.2±10.7 | 62.3±9.1 |
| LVEF <50%, n | 9 | 7 | 2 |
| RVEF (%) | 44.2±10 | 43.2±11 | 46.2±8 |
| LVEDD (mm) | 46.5±4 | 47.5±5 | 45.6±5 |
| CTG repeat length Kb | 2.1±1.5 | 2±1.6 | 2.4±1.3 |
Group 1 all patients without pacemaker in our global myotonic dystrophy (MD) population; group 2 patients excluded from the present study for different reasons explained in figure 1; group 3 patients enrolled in the study who underwent two electrophysiological studies. Group 1 versus group 2 versus group 3 not significant differences for all parameters.
AF, atrial fibrillation; CTG, cytosine-thymine-guanine; LVEDD, left ventricular end-diastolic dimension; LVEF, left ventricular ejection fraction; NSVT, non sustained ventricular tachycardia; RVEF, right ventricular ejection fraction.