Patient characteristics
| Total | No arrhythmia | Arrhythmia | p Value | |
|---|---|---|---|---|
| N | 166 | 96 | 70 | |
| Male | 49% | 49% | 50% | 0.895 |
| Mean current age (years) | 29.1 (±9.2) | 25.3 (±5.6) | 34.4 (±10.5) | <0.001 |
| Cardiac anatomy | 0.78 | |||
| Single LV: TA and DILV | 99 (60%) | 54 (56%) | 45 (64%) | |
| Single RV: MA, DIRV and HLHS | 23 (14%) | 15 (16%) | 8 (11%) | |
| PA+intact septum | 10 (6%) | 5 (5%) | 5 (7%) | |
| Unbalanced AVSD | 5 (3%) | 4 (4%) | 1 (1%) | |
| Heterotaxia | 20 (12%) | 13 (14%) | 7 (10%) | |
| Other | 9 (5%) | 5 (5%) | 4 (6%) | |
| Mean age at Fontan (years) | 9.0 (±8.5) | 6.4 (±5.4) | 12.6 (±10.5) | <0.001 |
| Median age at Fontan (years) | 5.6 (3.8–11.9) | 4.8 (3.3–7.6) | 11.0 (5.3–14.9) | |
| Type of Fontan | <0.001 | |||
| Modified AP | 104 (63%) | 48 (50%) | 56 (80%) | |
| Lateral tunnel | 22 (13%) | 17 (18%) | 5 (7%) | |
| TCPC | 40 (24%) | 31 (32%) | 9 (13%) | |
| Mean follow-up (years) | 18.6 (±4.7) | 17.3 (±3.7) | 20.5 (±5.2) | |
| Mortality | 21 (13%) | 9 (9%) | 12 (17%) | 0.21 |
The values are mean (±SD) or median (IQR). Categorical variables are presented as percentages.
AP, atriopulmonary connection; AVSD, atrioventricular septal defect; DILV, double inlet LV; DIRV, double inlet RV; HLHS, hypoplastic left heart syndrome; MA, mitral atresia; PA, pulmonary atresia; TA, tricuspid atresia; TCPC, extracardiac total cavopulmonary connection.