The above recommendations of the European Paediatric Pulmonary Vascular Disease Network relate to the grading system currently suggested by the European Society of Cardiology and the American Heart Association and are based on paediatric data only (class, LOE). The complete list of references on the above subtopic can be found in ref. 26.

CHD, congenital heart disease; COR, class of recommendation; LOE, level of evidence; MCV, mean corpuscular volume; PAH, pulmonary arterial hypertension; PDA, patent ductus arteriosus; PH, pulmonary hypertension; PPHVD, paediatric pulmonary hypertensive vascular disease; PVR, pulmonary vascular resistance; PVRI, PVR index; Qp, pulmonary blood flow; SVR, systemic vascular resistance; TIA, transient ischaemic attack; TPG, transpulmonary pressure gradient; TTE, transthoracic echocardiography; VSD, ventricular septal defect; WU, Wood units.