The above recommendations of the European Paediatric Pulmonary Vascular Disease Network relate to the grading system currently suggested by the European Society of Cardiology and the American Heart Association, and are based on paediatric data only (class, LOE). The complete list of references on the above subtopic can be found in ref. 23.

AVT, acute vasoreactivity testing; CHD, congenital heart disease; COR, class of recommendation; LOE, level of evidence; PAP, pulmonary artery pressure; PAH, pulmonary arterial hypertension; PH, pulmonary hypertension; PPHVD, paediatric pulmonary hypertensive vascular disease; PVRi, indexed pulmonary vascular resistance; RHC, right heart catheterisation; SVRi, indexed systemic vascular resistance.