Table 1

Patient data

				Mean pulmonary artery pressure (mm Hg)
	Age (years)/ sex	Diagnosis	Tris. 21	FiO₂=0.3	NO 40 FiO₂=0.3	PGI₂ 20 FiO₂>0.9	FiO₂=0.3	NO 40 FiO₂=0.3	FiO₂>0.9	NO 40 FiO₂>0.9	PGI₂ 20 FiO₂>0.9
Congenital heart disease
1	0.3/F	ASD VSD	No	48	44	42	4.3	3.3	1.6	1.3	1.4
2	0.3/M	VSD DORV	No	55	45	44	2.8	2.4	0.6	0.8	0.7
3	0.3/F	Truncus arteriosus	No	50	37	57	6.8	2.7	1.4	1.2	1.8
4	0.4/M	ASD VSD	No	39	33	25	3.8	3.3	2.7	2.9	1.6
5	0.4/F	AVSD	Yes	50	40	34	6.5	4.5	2.6	3.0	3.1
6	0.4/M	ASD VSD PDA	Yes	61	57	66	7.3	8.1	6.5	6.2	9.5
7	0.4/F	VSD PDA	Yes	64	71	53	7.7	7.8	3.5	7.5	2.4
8	0.5/F	VSD PDA	Yes	41	37	30	2.9	2.8	2.9	2.3	1.6
9	0.6/F	AVSD	Yes	39	37	31	5.5	4.8	1.2	1.2	0.8
10	0.8/F	VSD	Yes	41	36	32	2.9	2.8	2.6	1.6	1.4
11	1.1/M	ASD VSD PDA	Yes	43	39	47	5.4	4.0	2.9	2.8	2.6
12	3.0/F	Multiple VSDs	Yes	55	51	56	16	11.9	3.6	9.3	8.4
13	4.0/M	AOP window	No	62	61	66	4.9	3.5	3.4	3.8	5.4
14	7.2/M	Postop hemitruncus and VSD	No	57	38	36	8.1	6.3	5.1	5.1	5.9
15	12.8/F	VSD	Yes	54	52	45	8.9	10.0	7.7	6.7	6.7
16	13.6/F	VSD PDA	Yes	77	80	76	18.1	17.3	11.6	13.0	10.1
Mean	2.9			52	47	46	7.0	6.0	3.7	4.3	4.0
Other causes of pulmonary hypertension
17	1.1/F	BPD HAE PH	No	19	18	23	3.8	3.7	3.2	1.8	2.1
18	2.6/F	PPH	No	64	65	67	18.9	18.8	14.2	14.3	12.3
19	12.9/M	PPH	No	127	125	115	35.1	29.0	29.2	24.5	25.6
20	15.6/F	SLE PH	No	29	24	37	12.2	7.4	9.4	8.4	6.3
Mean	8.1			60	58	61	17.5	14.7	14.0	12.3	11.6

AOP window, aortopulmonary window; ASD, atrial septal defect; AVSD, atrioventricular septal defect; BPD, bronchopulmonary dysplasia; DORV, double outlet of right ventricle; HAE, high altitude exposure; PDA, patent ductus arteriosus; PH, pulmonary hypertension; PPH, primary pulmonary hypertension; SLE, systemic lupus erythematosus; VSD, ventricular septal defect.