Demographic features of the 55 subjects, classified by presence of GAA expansion
| Homozygous for GAA expansion | Normal allele | |
|---|---|---|
| Number | 45 | 10 |
| Age (years) | 30 (7) | 38 (6) |
| Age of onset of neurological disability (years) | 12 (5) | 16 (9) |
| Age at diagnosis (years) | 16 (6) | 19 (10) |
| Duration (years) | 17 (10) | 23 (11) |
| Age at which confined to wheelchair (years) | 19 (6) | 20 (7) |
Values are mean (SD). No significant differences were found between the groups.