Respiratory chain enzyme analysis in patient compared to 10 age matched controls for each complex. Values are expressed as a ratio to citrate synthase (nmol/min/unit citrate synthase)
| Patient | Control (mean (SD)) | |
|---|---|---|
| Complex I | 0.01 | 0.25 (0.06) |
| Complex II | 0.29 | 0.37 (0.09) |
| Complex III | 0.74 | 1.43 (0.28) |
| Complex IV | 0.16 | 1.31 (0.40) |