Table 1

Prenatal and postnatal anatomy of fetuses with right heart obstruction with intact ventricular septum, and outcome

Case		GA		Reason(s) for referral	Main diagnosis				Diagnosis of VCC		Shape of DA	Outcome^1-150
Case		GA		Reason(s) for referral	Prenatal	Confirmed			Prenatal	Confirmed	Shape of DA	Outcome^1-150
1	33	Small RV	PAIVS	PAIVS		na	Large	Sigmoid	Status: Fontan (7 years)
2	19	Small RV	PAIVS	—		Obvious	—	Unclear	Aborted
3	34	Small RV	PAIVS	PAIVS		Obvious	Large	Sigmoid	Status: BCPS (3 years)
4	31	Small RV, twin	PAIVS	PAIVS		Obvious	Large	Sigmoid	Status: BCPS (2 years)
5	20	Small RV	PAIVS	PAIVS, SAS, bicuspid AoV		Obvious	Large^1-151	Straight	Aborted; necropsy
6	19	Small RV	PAIVS	PAIVS		Obvious	—	Sigmoid	Aborted; necropsy
7	30	Small RV	PAIVS	PAIVS		Suspicious	Small	Straight	Status: BCPS (2 years)
8	38	Dandy-Walker	PAIVS	PAIVS		na	—	Unclear	Death
9	36	Small RV	PAIVS	PAIVS		Absent	Absent	Straight	Status: BCPS (2 years)
10	30	Small RV	PAIVS	PAIVS		Suspicious	Absent	Straight	Status: BT (1 year)
11	21	Small RV	PAIVS	PAIVS		na	—	Straight	Aborted; necropsy
12	24	Small RV	PAIVS	—		na	—	Straight	Aborted
13	17	Small RV	PAIVS	PAIVS		na	—	Straight	Aborted; dysmorphic fetus, by necropsy
14	22	Thickened RV	PAIVS	—		Absent	—	Straight	Aborted
15	24	Small RV	PAIVS	PAIVS		Absent	—	Sigmoid	Aborted
16	38	Small RV, family history	PAIVS	Severe duct dependent PS		na	Small	Straight	4p–deletion; death
17	27	Severe PS, family history	Severe PS	Severe duct dependent PS		Absent	Absent	Straight	Status: balloon valvuloplasty (1 year)
18	22	TTTS	Severe PS	Severe duct dependent PS		Absent	—	Straight	Ischaemic changes in brain; death
19	32	IDDM, previous stillborn	Severe PS	Moderate PS		na	Absent	Straight	Status: balloon valvuloplasty (6 years)
20	31	Previous stillborn (21 trisomy)	Severe PS	Moderate PS, ASD		Absent	Absent	Straight	Status: ASD closure, valvuloplasty (2 years)

AoV, aortic valve; ASD, atrial septal defect; BCPS, bidirectional cavopulmonary shunt; BT, Blalock-Taussig shunt; DA, ductus arteriosus; GA, gestational age (in weeks) at initial study; IDDM, insulin dependent diabetes mellitus; na, not assessed; PAIVS, pulmonary atresia and intact ventricular septum; PS, pulmonary stenosis; RV, right ventricle; SAS, subaortic stenosis; TTTS, twin to twin transfusion syndrome; VCC, ventriculocoronary connections.
↵1-150 Status is the patient’s postoperative status (at patient’s age). Death in all cases occurred after no active treatment (by parental request).
↵1-151 Probably large, as suggested by the presence of a dilated tortuous coronary artery found during necropsy. All other ventriculocoronary connections confirmations were by postnatal right ventriculography.