Table 1

Clinical and ECG findings useful for diagnosing right ventricular dysplasia/cardiomyopathy (RVD/C)

Familial history of RVD/C or premature sudden death
Clinical presentation
Ventricular arrhythmias (sometimes sudden death)
Right congestive heart failure
Supraventricular arrhythmias
Asymptomatic with abnormal ECG, chest x ray, or echocardiography
No specific physical findings (widely split II heart sound)
ECG abnormalities
T wave inversion on right precordial leads
ε waves (late potentials)
Prolonged QRS duration on V1–V2
Characteristics of ventricular arrhythmias
Frequently with LBBB pattern (right ventricular origin)
Wide range of severity (from patient to patient and during the course of disease) from sustained or non-sustained VT (rarely VF), to ventricular ectopic beats
  • LBBB, left bundle branch block; VT, ventricular tachycardia; VF, ventricular fibrillation.