Table 2

Mortality related to anatomical variation in pulmonary atresia associated with ventricular septal defect

Survival at 1 yearSurvival at end of study
Alive (n=45)Dead (n=15)p ValueAlive (n=32)Dead (n=28)p Value
MAPCAS
 Present246> 0.31911> 0.1
 Absent2191317
Pulmonary artery size1-150
 Absent32> 0.51-151 32> 0.61-151
 Reduced216> 0.71-152 1413> 0.61-152
 Normal2151511
Pulmonary arteries
 Confluent4013> 0.82825> 0.8
 Non-confluent5243
  • 1-150 Unknown in two cases.

  • 1-151 Absent + reduced v normal.

  • 1-152 Reduced v normal.

  • MAPCAS, major aortopulmonary collaterals.