Variable |
Number of patients or mean (SD), range |
Total population | 40 |
Aetiology | |
Idiopathic | 23 |
Other causes | 17 |
Anthracyclin | 7 |
Mitochondrial respiratory chain defect | 7 |
Postarrhythmia | 2 |
Postischaemia | 1 |
Age (years) | 7 (6), 3 months to 20 years |
Sex (male/female) | 21/19 |
Cardiothoracic index (%) | 57 (16) |
Indexed end diastolic diameter (mm/m2) | 67 (31), 31–163 |
Indexed end systolic diameter (mm/m2) | 56 (28), 23–147 |
Echocardiographic fractional shortening (%) | 17 (6), 8–27 |
Cardiac MIBG uptake (H/M ratio) | 1.67 (0.29), 1.1–2.2 |
MIBG washout rate (%) | 30 (11), 10–62 |
Plasma noradrenaline (pg/ml) | 249 (325) |
Follow up period (months) | 12 (10), 1–38 |
H/M ratio, heart to mediastinum activity ratio 4 hours after MIBG injection.