Table 1

Clinical and laboratory data in the study population

Variable Number of patients or
mean (SD), range
Total population40
Aetiology
 Idiopathic23
 Other causes17
 Anthracyclin7
 Mitochondrial respiratory chain defect7
 Postarrhythmia2
 Postischaemia1
Age (years)7 (6), 3 months to 20 years
Sex (male/female)21/19
Cardiothoracic index (%)57 (16)
Indexed end diastolic diameter (mm/m2)67 (31), 31–163
Indexed end systolic diameter (mm/m2)56 (28), 23–147
Echocardiographic fractional shortening (%)17 (6), 8–27
Cardiac MIBG uptake (H/M ratio)1.67 (0.29), 1.1–2.2
MIBG washout rate (%)30 (11), 10–62
Plasma noradrenaline (pg/ml)249 (325)
Follow up period (months)12 (10), 1–38
  • H/M ratio, heart to mediastinum activity ratio 4 hours after MIBG injection.