Characteristics of seven cases of primary leiomyosarcoma of the right ventricle
| Author | Age, sex, and clinical presentation | Diagnostic procedures | Non-cardiac presentation | Treatment and survival |
| Kennedy22 (1967) | 57, female, adenopathy deterioration of general condition, acute onset of dyspnoea | Negative angiography diagnosis at necropsy | Pulmonary, pleural, hepatic, pancreatic metastasis on necropsy | Radio- and chemotherapy. Died 17 months after diagnosis of adenopathy |
| Bearman5(1974) | 69, female, adenopathy acute RHF | Negative angiography negative echography diagnosis at necropsy | Pulmonary, renal, pancreatic metastasis at necropsy | No surgery, died 7 months after diagnosis of RHF |
| Burnett6 (1975) | 60, female, pericardial effusions causing tamponade | Negative angiography, negative pericardial biopsy diagnosis at necropsy | Pulmonary, hepatic metastasis at necropsy | No surgery, died several months after onset of symptoms |
| Talley et al 11(1986) | 46, male, RHF | Positive angiography, positive echography | None reported | Partial resection, died 10 months after onset of symptoms |
| Egloff et al 21 (1991) | 27, male, thoracic pain, systolic murmur, cough | Positive echography, positive CT | Pulmonary, pleural metastasis on chest x-ray | Complete resection. Still alive > 22 months after onset of symptoms |
| Panday et al 14 (1997) | 67, male, progressive dyspnoea, systolic murmur | Positive angiography, positive echography | None found | Complete resection. Still alive > 3 years after onset of symptoms |
| Willaert (present report) | 70, female, thoracic pain, progressive dyspnoea, systolic murmur | Positive echography, positive CT and MRI, peroperative diagnosis | None found | Complete resection. Relapse 7 months after surgery. Still alive 10 months after onset of symptoms |
Adapted from Egloff et al.21 CT, computed tomography; MRI, magnetic resonance imaging; RHF, right heart failure.