Table 1

Patient characteristics

Case Sex Age at diagnosis Age at death or HTx FS (%) EF (%) End point Mode of death Heart weight (g)
1M40401130HTx3501-150
2F52551020HTx560
3M22221738DeathHF635
4M19293327DeathSDNA
5M61611123HTxNA
6M54561830DeathHF850
7F26321935DeathSDNA
  • EF, ejection fraction; F, female; FS, fractional shortening; HF, progressive heart failure; HTx, heart transplantation; M, male; NA, not available; SD, sudden death.

  • 1-150 Weight after fixation.