Clinical studyCardiac conduction in myotonic dystrophy☆
References (31)
- et al.
Electrocardiographic abnormalities associated with myotonic dystrophy
Am Heart J
(1963) The heart and lungs in myotonic muscular dystrophy
Am J Med
(1962)- et al.
The effect of diphenylhydantoin on atrioventricular and intraventricular conduction in man
Am Heart J
(1970) - et al.
“Normal” atrioventricular conduction
Am J Med
(1970) - et al.
Site of conduction disturbances in a family with myotonic dystrophy
Am J Cardiol
(1973) - et al.
Conduction disturbances of the left bundle branch system and their relationship to complete heart block
Am J Med
(1971) - et al.
Prolonged atrial flutter in myotonic dystrophy
Am J Cardiol
(1962) - et al.
Natural history of combined right bundle block and left anterior hemiblock (bilateral bundle branch block)
Am J Med
(1973) - et al.
Dystrophia Myotonica and Related Disorders
The heart in myotonia atrophica
Br Heart J
(1951)
A-V dissociation in dystrophia myotonica
Br Heart J
The heart in myotonia atrophica
Arch Intern Med
Genetic Disorders of Man
The effects of procaine amide on atrioventricular and intraventricular conduction in man (abstract)
Circulation
Drugs used in the chemotherapy of malaria
Cited by (84)
Skeletal Muscle Channelopathies
2018, NeurotherapeuticsReduced renal function in patients with Myotonic Dystrophy type 1 and the association to CTG expansion and other potential risk factors for chronic kidney disease
2017, Neuromuscular DisordersCitation Excerpt :This phenomenon called anticipation leads to increasing disease severity and decreasing age at onset in the next generation [1]. DM1 affects several organs, apart from classic features as myotonia, muscle weakness and early cataract, heart, central nervous system, gastrointestinal tract and endocrine system are frequent targets of the disease [2–6]. To our knowledge, renal function in patients with DM1 has been measured and evaluated only in a few cases [7] but there are previous studies where creatinine levels and estimations of renal function have been studied [8].
Muscle channelopathies
2014, Neurologic ClinicsCitation Excerpt :Physicians rely on off-label use of antiepileptic, anesthetic, and antiarrhythmic drugs to treat myotonia (see Table 1). Anecdotal data support the use of quinine,57 procainamide,57,58 and phenytoin58 in patients with myotonia. There is also evidence for class 1B antiarrhythmics, tocainide (withdrawn from the market) and mexiletine, which may be more effective than quinine, procainamide, or phenytoin for autosomal recessive myotonia and PMC.17,59
Nondystrophic myotonia: Challenges and future directions
2014, Experimental NeurologyPatients with neuromuscular disorder
2013, Medical Clinics of North AmericaCitation Excerpt :There are also reports of paroxysmal complete heart block. Patients with myotonic dystrophy should receive an ECG at least annually, and especially before surgery.94 Patients with myotonic dystrophy have delayed gastric emptying, and this has been shown even in patients without gastrointestinal symptoms.
When do you implant a pacemaker in Myotonic Dystrophy?
2011, Presse Medicale
- ☆
This study was supported by a grant from the Muscular Dystrophy Associations of America, Inc., and Grant RR00044 from the U.S. Public Health Service. These studies were presented in part at the meetings of the American Academy of Neurology and American College of Physicians, April 1973.
- ∗
Recipent of an American College of Physicians Teaching and Research Scholarship.
- 1
From the Departments of Neurology and Medicine, University of Rochester, School of Medicine and Dentistry, Rochester, New York.
- †
Present address: 939 Ridgeland Street, Cheyenne, Wyoming 82001.
- §
Present address: 124 Pebblebeach Drive, Springfield, Illinois 62704.