The case of a 66-year-old woman with myotonic dystrophy is presented. This patient underwent implantation of an insertable loop recorder as a participant in a clinical trial. At 1-month follow-up, interrogation of the insertable loop recorder revealed multiple episodes of wide complex tachycardia. She underwent electrophysiologic study, which revealed moderate His-Purkinje disease, focal atrial tachycardia, monomorphic ventricular tachycardia, and ventricular fibrillation. Successful radiofrequency ablation of the focal atrial tachycardia and implantation of a dual-chamber implantable cardioverter defibrillator was performed.