Abstract
An acquired form of cor triatriatum, resulting in significant supramitral valve obstruction, complicating a pediatric orthotopic heart transplantation was diagnosed by transesophageal echocardiography. Surgical resection of the hypertrophied atrial septum and atrial wall corrected the anatomic obstruction and improved the hemodynamics.
MeSH terms
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Adolescent
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Anastomosis, Surgical
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Cardiomyopathy, Hypertrophic / diagnostic imaging
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Cardiomyopathy, Hypertrophic / pathology
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Cardiomyopathy, Hypertrophic / surgery*
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Child
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Cor Triatriatum / diagnostic imaging
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Cor Triatriatum / pathology
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Cor Triatriatum / surgery*
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Echocardiography, Doppler
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Echocardiography, Transesophageal
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Female
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Heart Atria / diagnostic imaging
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Heart Atria / pathology
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Heart Atria / surgery*
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Heart Septum / diagnostic imaging
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Heart Septum / pathology
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Heart Septum / surgery
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Heart Transplantation / methods*
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Hemodynamics / physiology
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Humans
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Male
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Postoperative Complications / diagnostic imaging
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Postoperative Complications / pathology
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Postoperative Complications / surgery*
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Reoperation
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Suture Techniques
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Ventricular Function, Right / physiology