Abstract
"Spongy left ventricular myocardium," or noncompaction of left ventricular myocardium, is a rare disorder of endomyocardial morphogenesis. It is usually seen in the pediatric population and is often associated with other congenital cardiac malformations. We describe an adult with noncompaction of left ventricular myocardium without associated congenital cardiac anomalies.
MeSH terms
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Adolescent
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Biopsy
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Coronary Angiography
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Follow-Up Studies
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Heart Defects, Congenital / complications*
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Heart Defects, Congenital / diagnosis
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Heart Defects, Congenital / physiopathology
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Heart Ventricles / abnormalities*
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Heart Ventricles / diagnostic imaging
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Heart Ventricles / physiopathology
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Humans
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Magnetic Resonance Imaging
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Male
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Myocardium / pathology*
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Stroke Volume
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Ventricular Dysfunction, Left / diagnosis
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Ventricular Dysfunction, Left / etiology*
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Ventricular Dysfunction, Left / physiopathology