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Acquired coarctation of the aorta in William’s syndrome
  1. R Dhillon,
  2. T D Reddy,
  3. A Redington
  1. Department of Paediatric Cardiology, Royal Brompton Hospital, London SW3 6NP, UK
  1. Dr Dhillon.

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The arterial lesions of William’s syndrome are characteristic1: supravalvar aortic stenosis, coarctation of the aorta, peripheral pulmonary artery stenosis, and stenosis of the renal and coronary arteries. The development of slowly progressive coarctation has been described in only one patient,2 ,3 in whom angiography at 3 years of age showed a diffusely hypoplastic ascending aorta but no coarctation. Seven years later, angiography showed long segment coarctation distal to the left subclavian artery. We describe a patient in whom coarctation of the aorta developed over a much shorter time period.

Case report

William’s syndrome was diagnosed in this boy at the age of 4 years on the basis of “elfin facies” comprising epicanthic folds, a shallow nasal bridge, anteverted nares, long philtrum, and prominent lips.4 …

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