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Isolated left ventricular apical hypoplasia: a new congenital anomaly described with cardiac tomography
  1. M Fernandez-Valls1,
  2. M B Srichai1,2,*,
  3. A E Stillman1,
  4. R D White1,
  1. 1Department of Radiology (Section of Cardiovascular Imaging), Cleveland Clinic Foundation, Cleveland, Ohio 44195, USA
  2. 2Department of Cardiovascular Medicine, Cleveland Clinic Foundation
  1. Correspondence to:
    Dr R D White
    Section of Cardiovascular Imaging, Desk Hb6, Cleveland Clinic Foundation, 9500 Euclid Avenue, Cleveland, Ohio 44195, USA;


Objective: To describe cardiac tomography findings of an apparently new, presumably congenital, left ventricular (LV) abnormality noted consistently in three patients.

Patients: Three patients presenting with non-specific symptoms including fatigue, shortness of breath, or chest discomfort were evaluated with cardiac tomography for cardiac structure and function.

Results: Findings from the three patients were very similar: a truncated and spherical LV with abnormal diastolic and systolic function, invagination of fatty material into the myocardium of the defective LV apex, origin of a complex papillary network in the anteroapical LV, and an elongated right ventricle wrapping around the deficient apex.

Conclusions: Isolated LV apical hypoplasia is a unique, presumably congenital, cardiac anomaly that is an important condition to recognise.

  • congenital heart disease
  • magnetic resonance imaging
  • multidetector computed tomography
  • CT, computed tomography
  • LV, left ventricular
  • MDCT, multidetector computed tomography
  • MRI, magnetic resonance imaging
  • RV, right ventricle

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  • Also at Department of Cardiovascular Medicine, Cleveland Clinic Foundation

  • * Unrestricted training support from Berlex Laboratories, Pine Brook, New Jersey, USA.