Abstract

Ruptured aneurysms of the sinus of Valsalva with a gigantic fistulous tract are extremely rare. A single origin of the coronary arteries is a rare coronary anomaly. We describe the case of a 6-year-old girl who had a ruptured aneurysm of the right coronary sinus with a gigantic fistulous tract and an anomalous origin of the right coronary artery. Transthoracic echocardiography showed the right coronary artery (RCA) aneurysm and RCA fistula connecting to the right ventricular (RV). Aortography revealed the presence of a right coronary sinus of Valsalva aneurysm (SVA)-RV fistula and the originating of right coronary artery (RCA) from left circumflex artery (LCX). She was diagnosed as having a gigantic SVA to right ventricle fistula and a single origin of the coronary arteries. Successful trancatheter closure of the fistulous ostium was performed.