RT Journal Article
SR Electronic
T1 Primary cardiac amyloidosis in a young man presenting with angina pectoris.
JF British Heart Journal
JO Heart
FD BMJ Publishing Group Ltd and British Cardiovascular Society
SP 233
OP 236
DO 10.1136/hrt.52.2.233
VO 52
IS 2
A1 S Saltissi
A1 P J Kertes
A1 D G Julian
YR 1984
UL http://heart.bmj.com/content/52/2/233.abstract
AB A 32 year old man presenting with typical angina pectoris was found to have primary cardiac amyloidosis. Myocardial infiltration was strongly suggested by echocardiography, and a histological diagnosis was confirmed by renal biopsy. Nevertheless, technetium pyrophosphate myocardial scanning, recently proposed as a sensitive non-invasive test, showed negative results despite widespread cardiac involvement confirmed at necropsy after unexpected sudden death. Postmortem findings also showed subintimal amyloid material in a severely narrowed right coronary artery. This case highlights several unusual clinical features in a patient with advanced primary cardiac amyloidosis.