PT - JOURNAL ARTICLE AU - Yuji Ikari AU - Kenji Kuwako AU - Tetsu Yamaguchi TI - Fabry's disease with complete atrioventricular block: histological evidence of involvement of the conduction system AID - 10.1136/hrt.68.9.323 DP - 1992 Sep 01 TA - British Heart Journal PG - 323--325 VI - 68 IP - 9 4099 - http://heart.bmj.com/content/68/9/323.short 4100 - http://heart.bmj.com/content/68/9/323.full SO - Heart1992 Sep 01; 68 AB - A 63 year old man with complete atrioventricular block was diagnosed as having Fabry's disease. A short PR interval is a common electrocardiographic finding in Fabry's disease, but complete atrioventricular block is a very rare complication. Necropsy indicated that lipid accumulation in the atrioventricular conduction system was the probable cause of this patient's atrioventricular block.