RT Journal Article
SR Electronic
T1 The unravelling of primary myocardial impairment in Marfan syndrome by modern echocardiography
JF Heart
JO Heart
FD BMJ Publishing Group Ltd and British Cardiovascular Society
SP 1561
OP 1566
DO 10.1136/hrt.2008.152934
VO 95
IS 19
A1 A Kiotsekoglou
A1 G R Sutherland
A1 J C Moggridge
A1 D K Nassiri
A1 A J Camm
A1 A H Child
YR 2009
UL http://heart.bmj.com/content/95/19/1561.abstract
AB Use of echocardiography has dramatically changed the way in which patients with Marfan syndrome are diagnosed, monitored and treated. Owing to the lethal nature of aortic complications, priority has been given to the assessment of the aortic root. Echocardiographic studies on patients with Marfan syndrome have also provided data supporting primary myocardial involvement, although this evidence has remained controversial for several years. Use of more sensitive ultrasound techniques has demonstrated mild myocardial impairment in these patients. Biventricular function assessment should be added to the aortic root evaluation, so that appropriate treatment may be offered to support myocardial function.