Table 3

 Follow up data

Data are mean (SD) or median (range).
Echocardiography
    Ascending aortic velocity (m/s)1.9 (0.57)
    Descending aortic velocity (m/s))2.2 (0.51)
    Echocardiographic gradient (mm Hg)6.1 (7.8)
    Time to half peak diastolic velocity (m/s)70 (14)
    Femoral pulses (grade)4 (3–4)
Blood pressure
    Upper limb systolic (mm Hg)109 (14)
    Upper limb diastolic (mm Hg)58 (10)
    Lower limb systolic (mm Hg)123 (17.5)
    Lower limb diastolic (mm Hg)68 (12.5)
    Upper limb systolic centile (mm Hg)75 (20)
    Upper to lower limb gradient (mm Hg)−15 (17.6)