Table 1

 Familial causes of sudden death

Clinical utility in screening
ECGEchoGenotype
Scoring ranges from − (no help) through ±, +, ++, +++ (very helpful). See text for details.
Structural abnormalities
    Hypertrophic cardiomyopathy+++++
    Dilated cardiomyopathy++++
    Marfan syndrome+++
    Arrhythmogenic right ventricular cardiomyopathy+
Primary electrical abnormalities
    Long QT syndrome+++++
    Catecholaminergic polymorphic ventricular tachycardia±+
    Brugada syndrome±+