Baseline clinical, ECG and echocardiographic characteristics according to modality of diagnosis
| Overall (n = 65) | Symptom-based diagnosis (n = 48) | Non-symptom-based diagnosis (n = 17) | p Value* | |
|---|---|---|---|---|
| Data are mean (SD) or number (%). | ||||
| *Comparison between subgroups with symptom-based and non-symptom-based diagnosis. | ||||
| LV, left ventricular. | ||||
| Age at first evaluation (years) | 45 (16) | 49 (15) | 35 (15) | 0.002 |
| Age at initial diagnosis of myocardial disease (years) | 42 (17) | 45 (17) | 34 (16) | 0.023 |
| Familial occurrence | 20 (31%) | 8 (17%) | 12 (71%) | NA |
| Neuromuscular disease | 6 (9%) | 3 (6%) | 3 (18%) | 0.36 |
| Left bundle branch block | 21 (32%) | 20 (42%) | 1 (6%) | 0.016 |
| Normal ECG | 8 (12%) | 3 (6%) | 5 (29%) | 0.04 |
| LV end diastolic diameter (mm) | 67 (11) | 69 (12) | 62 (11) | 0.04 |
| LV ejection fraction (%) | 31 (11) | 28 (10) | 39 (11) | <0.001 |
| Left atrial size (mm) | 47 (10) | 50 (9) | 41 (8) | <0.001 |
| Moderate or severe mitral regurgitation | 35 (54%) | 29 (60%) | 6 (35%) | 0.13 |
| Number of non-compacted segments | 6 (3) | 5 (3) | 6 (2) | 0.2 |
| Ratio of non-compacted to compacted segments | 2.7 (0.7) | 2.8 (0.7) | 2.7 (0.6) | 0.6 |
| Transmitral restrictive pattern | 21 (32%) | 19 (40%) | 2 (12%) | 0.07 |