38F | 1. Correction (1970) | 1. Typical AFlutter (macro) 2. & 3. Crista terminalis AT (focal) 4. Septal His AT (focal) | PVR + RA Maze procedure (2/01). AAIR pacemaker (3/06) – atrial standstill + junctional escape rhythm (30 bpm) | 2 × ATs post-PVR. 1 × AFlutter post pacemaker (metoprolol) but symptomatically improved. FAILURE (14 months) |
22M | 1. Correction (1985) | 1. IVC septum AT (focal) 2. Coronary sinus os floor AT (focal) | PVR + RA microwave ablation (2/04) | Recurrent AT post-RFA. No arrhythmia post-PVR (amiodarone). Partial success (31 months) |
37M | 1. Brock (1967) 2. Correction (1971) | 1. Typical AFlutter (macro) 2. High right atrium/RAA AT (micro) 3. Crista terminalis AT (micro) | Nil | Recurrence of AT post-RFA (suppressed with amiodarone). Partial success (29 months) |
37F | 1. Correction (1975) 2. TVR (1981) 3. Redo TVR (2001) | 1. Typical AFlutter (macro) 2. Tricuspid valve annulus AT (focal) 3. Multiple non-sustained ATs | DDDRP pacemaker (6/05) – sinus node disease. AV node RFA (10/05) | Recurrence of AT post-RFA. Fewer palpitations post-pacemaker (no antiarrhythmic therapy). Partial success (lost to follow-up) |
39M | 1. Brock (1968) 2. Correction (1971) 3. Cryosurgery for VT (1992) 4. PVR + RA microwave ablation (8/04) | 1. Cranial crista terminalis AT (micro) | Nil | Incessant AT post-PVR. No arrhythmia post-RFA (no antiarrhythmic therapy). Complete success (26 months) |
43F | 1. Correction (1969) - post op CHB (paced) | 1. Posterior IVC AT (focal) 2. Coronary sinus os floor AT (focal) 3. Incisional AT (RAA–base of RA–IVC) (macro) | Pacemaker upgrade to DDDRP (12/05) | AT post-RFA and post-DDDRP upgrade (suppressed with metoprolol + flecainide). Partial success (1 month) |
46F | 1. Pott’s anastomosis (1955) 2. Brock (1967) 3. Correction (1976) | 1. Typical AFlutter (macro) 2. Low lateral right AT (focal) 3. Crista terminalis AT (focal) 4. Coronary sinus os AT (focal) | RVOT conduit replacement, TVR, debulking of RV + cryoablation (10/02) | AT recurred post-RFA (3/02) – asymptomatic. New onset AF 45 months post-surgery (7/06) (started on sotalol). Failure (45 months) |
27F | 1. Brock (1973) 2. Correction (1975) 3. Replacement of RVOT conduit (1986) | 1. Typical AFlutter (macro) 2. Low crista terminalis AT (focal) 3. Mitral valve annulus AT (focal) | DDDRP pacemaker (5/04) – sinus node disease | Recurrence of AT post-RFA + new paroxysmal AF. No arrhythmia post-pacemaker (atenolol + verapamil). Partial success (28 months) |
44F | 1. Correction (1971) | 1. Typical AFlutter (macro) | DDDRP pacemaker (7/05) – sinus & AV node disease. PVR + cryoablation RVOT (9/05) | No arrhythmia post-RFA (metoprolol). Complete success (14 months) |
42M | 1. Correction (1968) | 1. Typical AFlutter (macro) 2. Crista terminalis AT (macro) 3. Septal AT (macro) 4. RAA AT (focal) | Nil | No arrhythmia post-RFA (metoprolol). Complete success (19 months) |