Table 1 Demographics for cases with IPAH seen between April 2001 and March 2006
MeanSDRangeNo
Number of cases60
Age at presentation (years)7.375.70.07–19.7
Male (%)23 (38%)
WHO functional class3.330.552–4
PAPm (mm Hg)61.920.231–150
SAPm (mm Hg)62.912.443–95
RAPm (mm Hg)7.693.73–18
CI (l/min−1.m−2)2.71.031.3–5.4
PVR (U/m2)22.0110.95.6–43.3
Treatment at closure of study or death or transplant
Epoprostenol6
Bosentan12
Sildenafil7
Epoprostenol + bosentan and/or sildenafil22
Bosentan + sildenafil7
Nifedipine4
Nil2
Transplanted6
Died11
  • CI, contrast intensity; PAPm, mean pulmonary artery pressure; PVR, pulmonary vascular resistance; RAPm, mean right atrial pressure; SAPm, mean stable angina pectoris.