Infant mortality of congenital heart defects: the EPICARD study
| ACC-CHD categories | N | Mortality | 95% CI | |||
| ≤7 days | 8–28 days | 29 days–1 year | Infant mortality | |||
| % | % | % | % | |||
| 1. Heterotaxy, including isomerism and mirror-imagery | 8 | 25.0 | 0.0 | 12.5 | 37.5 | 8.5 to 75.5 |
| 2. Anomalies of the venous return | 26 | 3.9 | 11.5 | 11.5 | 26.9 | 11.6 to 47.8 |
| 3. Anomalies of the atria and interatrial communications | 174 | 0.6 | 0.6 | 2.3 | 3.5 | 1.3 to 7.3 |
| 4. Anomalies of the atrioventricular junctions and valves | 109 | 8.3 | 7.3 | 12.8 | 28.4 | 20.2 to 37.9 |
| 5. Complex anomalies of atrioventricular connections | 7 | 0.0 | 0.0 | 14.3 | 14.3 | 0.4 to 57.9 |
| 6. Functionally univentricular hearts | 48 | 41.7 | 12.5 | 4.1 | 58.3 | 43.2 to 72.4 |
| 7. Ventricular septal defects (VSD) | 1395 | 0.2 | 0.5 | 0.9 | 1.6 | 1.0 to 2.4 |
| 8. Anomalies of the ventricular outflow tracts | 447 | 2.3 | 2.0 | 4.0 | 8.3 | 5.9 to 11.2 |
| 9. Anomalies of the extrapericardial arterial trunks | 125 | 3.2 | 6.4 | 2.4 | 12.0 | 6.9 to 19.0 |
| 10. Congenital anomalies of the coronary arteries | 9 | 0.0 | 0.0 | 11.1 | 11.1 | 0.3 to 48.2 |
| All | 2348 | 2.1 | 1.8 | 2.5 | 6.4 | 5.5 to 7.5 |
| All, excluding cases associated with chromosomal anomalies | 2204 | 1.7 | 1.2 | 2.1 | 5.0 | 4.2 to 6.0 |
| All, excluding cases associated with chromosomal anomalies or genetic syndromes | 2148 | 1.5 | 1.1 | 1.8 | 4.4 | 3.5 to 5.3 |
| All, excluding cases associated with chromosomal, genetic or other anomalies | 1889 | 1.2 | 0.9 | 1.5 | 3.6 | 2.8 to 4.6 |
| All, excluding cases associated with chromosomal, genetic syndromes or other anomalies and IVSD* | 783 | 2.9 | 2.2 | 3.6 | 8.7 | 6.8 to 10.9 |
↵* Isolated ventricular septal defects.