Table 1

Distribution of categories of congenital heart defects (ACC-CHD^*) and associated anomalies: the EPICARD study

ACC-CHD categories	N	Total		N	Live births
ACC-CHD categories	N	% Chromosomal anomalies	% Anomalies of other systems^†	N	% Chromosomal anomalies	% Anomalies of other systems^†
1. Heterotaxy, including isomerism and mirror-imagery	37	0.0	24.3	8	0.0	25.0
2. Anomalies of the venous return	31	19.4	16.1	26	7.7	15.4
3. Anomalies of the atria and interatrial communications	182	9.9	19.8	174	7.5	19.0
4. Anomalies of the atrioventricular junctions and valves	213	57.3	12.7	109	43.1	13.8
5. Complex anomalies of atrioventricular connections	13	0.0	7.7	7	0.0	0.0
6. Functionally univentricular hearts	158	15.8	19.6	48	8.3	20.8
7. Ventricular septal defects (VSD)	1491	9.3	11.1	1395	3.9	11.0
8. Anomalies of the ventricular outflow tracts	563	10.7	19.1	447	4.5	14.3
9. Anomalies of the extrapericardial arterial trunks	170	15.9	31.2	125	3.2	26.4
10. Congenital anomalies of the coronary arteries	9	0.0	0.0	9	0.0	0.0
All	2867	13.8	15.2	2348	6.1	13.4

↵* Anatomic and clinical classification of congenital heart defects (Houyel et al, 2011).
↵† Excluding chromosomal anomalies.