Total and live birth prevalence of congenital heart defects: the EPICARD
| ACC-CHD categories | N | LB | TOP | SB | Prevalence (per 10 000) | |||
| % | % | % | Total* | 95% CI | Live birth† | 95% CI | ||
| 1. Heterotaxy, including isomerism and mirror-imagery | 37 | 21.6 | 75.7 | 2.7 | 1.2 | 0.8 to 1.6 | 0.2 | 0.1 to 0.5 |
| 2. Anomalies of the venous return | 31 | 83.9 | 16.1 | 0.0 | 1.0 | 0.7 to 1.4 | 0.8 | 0.5 to 1.2 |
| 3. Anomalies of the atria and interatrial communications | 182 | 95.6 | 4.4 | 0.0 | 5.7 | 4.9 to 6.6 | 5.5 | 4.7 to 6.4 |
| 4. Anomalies of the atrioventricular junctions and valves | 213 | 51.2 | 42.7 | 6.1 | 6.7 | 5.8 to 7.7 | 3.5 | 2.8 to 4.2 |
| 5. Complex anomalies of atrioventricular connections | 13 | 53.8 | 46.2 | 0.0 | 0.4 | 0.2 to 0.7 | 0.2 | 0.1 to 0.5 |
| 6. Functionally univentricular hearts | 158 | 30.4 | 62.7 | 6.9 | 5.0 | 4.2 to 5.8 | 1.5 | 1.1 to 2.0 |
| 7. Ventricular septal defects (VSD) | 1491 | 93.6 | 5.7 | 0.7 | 47.0 | 44.6 to 49.4 | 44.4 | 42.1 to 46.8 |
| 8. Anomalies of the ventricular outflow tracts | 563 | 79.4 | 18.5 | 2.1 | 17.7 | 16.3 to 19.3 | 14.2 | 12.9 to 15.6 |
| 9. Anomalies of the extrapericardial arterial trunks | 170 | 73.5 | 23.5 | 3.0 | 5.3 | 4.6 to 6.2 | 4.0 | 3.3 to 4.7 |
| 10. Congenital anomalies of the coronary arteries | 9 | 100.0 | 0.0 | 0.0 | 0.3 | 0.1 to 0.5 | 0.3 | 0.1 to 0.5 |
| All | 2867 | 81.9 | 16.3 | 1.8 | 90.3 | 87.0 to 93.6 | 74.8 | 71.8 to 77.8 |
| All, excluding cases associated with chromosomal anomalies | 2471 | 89.2 | 9.8 | 1.0 | 77.8 | 74.8 to 80.9 | 68.4 | 67.3 to 73.2 |
| All, excluding cases associated with chromosomal or other anomalies | 2036 | 92.8 | 6.4 | 0.8 | 64.1 | 61.4 to 67.0 | 60.2 | 57.5 to 62.9 |
| All, excluding cases associated with chromosomal or other anomalies and IVSD‡ | 930 | 84.2 | 14.0 | 1.8 | 29.3 | 27.4 to 31.2 | 24.9 | 23.2 to 26.7 |