Table 2

Baseline demographic and clinical characteristics of the patients with Eisenmenger syndrome from the own institution. All patients were treatment naïve. Patients were censored at the time of commencing disease targeting therapies. This cohort is identical to the treatment naïve subgroup included in a previous publication by Dimopoulos et al11

n (%)
Age, years34.5±12.7
% Male79 (36%)
% Down syndrome66 (30%)
Cardiac defect
 Pretricuspid21 (9.6%)
 Post-tricuspid89 (40.7%)
 Complex99 (45.4%)
 Others10 (4.6%)
Oxygen saturation in air %83.9 ±8.7%
NYHA Class
 I/II105 (47.9%)
 III/IV114 (52.1%)
  • NYHA, New York Heart Association.