Table 1

Demographics of the patients with cyanotic congenital heart disease

Clinical characteristicsN=98
Female gender, N (%)55 (56)
Age, years40±14
Saturation, %83±7
Diagnoses
Eisenmenger syndrome, N (%)69 (70)
 Ventricular septal defect, N47
 Atrial septal defect, N12
 Atrioventricular septal defect, N5
 Persistent ductus arteriosus, N4
 Aortopulmonary window, N1
Pulmonary arteriovenous malformation, N (%)2 (2)
Univentricular heart, N (%)17 (18)
Pulmonary atresia, ventricular septal defect and major aortopulmonary collateral arteries, N (%)9 (9)
Ebstein anomaly with atrial septal defect, N (%)1 (1)
Down syndrome, N (%)14 (14)
22q11.2 deletion syndrome (DiGeorge syndrome), N (%)6 (6)
Pulmonary hypertension*, N (%)83 (85)
Medical history
Previous history of thrombosis, N (%)20 (20)†
Brain, N13
Heart, N1
Lung, N6
Arm/leg, N1
Atrial flutter/fibrillation, N (%)24 (24)
Paroxysmal, N (%)18 (18)
Permanent, n (%)6 (6)
Pacemaker, n (%)7 (7)
Iron deficiency, n (%)32 (33)
Previous phlebotomy, n (%)32 (33)
Previous cardiac surgery, N (%)19 (20)
Medication
Iron treatment, n (%)12 (12)
Antiplatelet/coagulation medicine, n (%)33 (34)‡
Aspirin, n (%)15 (16)
Clopidogrel, n (%)1 (1)
Warfarin, n (%)15 (16)
Marcoumar, n (%)6 (6)
  • The results are shown as mean±SD or actual number and percentage.

  • *Pulmonary hypertension had previously been verified by right heart catheterisation.

  • †Some of the patients had had more than one thrombosis.

  • ‡Some of the patients received more than one antiplatelet/coagulation medicine.