TableĀ 3

Panama classification of Paediatric Pulmonary Hypertensive Vascular Disease (PPHVD) (2011): 10 basic categories of PPHVD

CategoryPPHVD category
1Prenatal or developmental pulmonary hypertensive vascular disease
2Perinatal pulmonary vascular maladaptation
3Paediatric cardiovascular disease
4Bronchopulmonary dysplasia
5Isolated paediatric pulmonary hypertensive vascular disease (isolated paediatric pulmonary arterial hypertension)
6Multifactorial pulmonary hypertensive vascular disease in congenital malformation syndromes
7Paediatric lung disease
8Paediatric thromboembolic disease
9Paediatric hypobaric hypoxic exposure
10Paediatric pulmonary vascular disease associated with other system disorders
  • From Cerro et al.4