Characteristics of patients with a Fontan circulation (n=34) undergoing heart transplantation
| Fontan patients (n=34) | |
|---|---|
| Age—median years (IQR) | 17 (11–31), range 4–51 |
| Blood group | |
| O | 17 (50) |
| A | 10 (29) |
| B | 4 (12) |
| AB | 3 (9) |
| Ventricular morphology | |
| LV dominant | 19 (56) |
| RV dominant | 15 (44) |
| Diagnoses | |
| Atrioventricular septal defect | 3 (9) |
| Double-inlet LV | 6 (18) |
| Double-outlet RV | 8 (24) |
| Hypoplastic left heart syndrome | 5 (15) |
| Transposition of the great arteries | 5 (15) |
| Tricuspid atresia | 7 (21) |
| Dextrocardia | 4 (12) |
| Situs inversus | 1 (3) |
| Left atrial isomerism | 2 (6) |
| Right atrial isomerism | 1 (3) |
| Time since Fontan (years)—mean (SD) | 11.5 (9.1), range: 0.23–33 |
| Type of Fontan | |
| ECC | 16 (47) |
| AP | 14 (41) |
| LT | 4 (12) |
| Fenestration | 10 (29) |
| Fenestration closure prior to Tx | 3 (9) |
| Number of prior surgeries—mean (SD) | 2.7 (1.1) |
| Bidirectional cavopulmonary connection | 13 (38) |
| Blalock–Taussig shunt | 5 (15) |
| Norwood procedure | 5 (15) |
| PLE | 5 (15) |
| Plastic bronchitis | 1 (3) |
| Pulmonary AVM | 1 (3) |
| History of atrial arrhythmia | 8 (24) |
AP, atriopulmonary Fontan; AVM, arteriovenous malformation; ECC, extracardiac conduit; IQR, interquartile range; LT, lateral tunnel Fontan; LV, left ventricle; PLE, protein-losing enteropathy; RV, right ventricle; Tx, transplantation.