BAV morphology | n (%) | RCA above ST | LCA above ST | ||
Inflow and septal defects | PLSCV | Total Type 1A Type 1B Type 2A Type 2B Type 3A Type 3B | 15 6 (40%) 2 (13%) 3 (20% 1 (7%) 1 (7%) 2 (13%) | 3 3 (100%) 0 (0%) 0 (0%) 0 (0%) 0 (0%) 0 (0%) | 4 1 (25%) 0 (0%) 1 (25%) 0 (0%) 1 (25%) 1 (25%) |
Muscular VSD | Total Type 1A Type 1B Type 2A Type 3A Type 3B | 20 12 (60%) 5 (25%) 0 (0%) 2 (10%) 1 (5%) | 3 1 (33%) 1 (33%) 0 (0%) 1 (33%) 0 (0%) | 8 5 (62%) 2 (25%) 0 (0%) 1 (13%) 0 (0%) | |
ASD | Total Type 1A Type 1B Type 2A Type 3A | 11 5 (46%) 3 (27%) 2 (18%) 1 (9%) | 2 2 (100%) 0 (0%) 0 (0%) 0 (0%) | 5 2 (40%) 2 (40%) 0 (0%) 1 (20%) | |
AVSD | Total Type 1A Type 2A Type 2B | 4 2 (50%) 1 (25%) 1 (25%) | 1 1 (100%) 0 (0%) 0 (0%) | 2 0 (0%) 1 (50%) 1 (50%) | |
AV valve anomalies TV dysplasia TV hypoplasia TV absent | Total Type 1A Type 1B Type 2A | 11 5 (46%) 3 (27%) 3 (27%) | 2 1 (50%) 1 (50%) 0 (0%) | 3 1 (33%) 1 (33%) 1 (33%) | |
Total Type 1A Type 1B Type 2A | 3 1 (33%) 1 (33%) 1 (33%) | 1 1 (100%) 0 (0%) 0 (0%) | 1 1 (100%) 0 (0%) 0 (0%) | ||
Total Type 1A | 1 1 (100%) | 0 0 (0%) | 0 0 (0%) | ||
MV hypoplasia MV dysplasia MV atresia | Total Type 1A Type 1B Type 2A Type 2B Type 3A | 24 12 (50%) 6 (25%) 2 (8%) 1 (4%) 3 (13%) | 4 3 (75%) 0 (0%) 1 (25%) 0 (0%) 0 (0%) | 8 4 (50%) 2 (25%) 0 (0%) 1 (12.5%) 1 (12.5%) | |
Total Type 1A Type 2B | 5 4 (80%) 1 (20%) | 0 0 (0%) 0 (0%) | 0 0 (0%) 0 (0%) | ||
Total Type 1A | 1 1 (100%) | 0 0 (0%) | 0 0 (0%) | ||
Outflow defects and LV hypoplasia | Perimembranous VSD | Total Type 1A Type 1B Type 2A Type 2B Type 3A Type 3B | 22 10 (45%) 4 (18%) 5 (22%) 1 (5%) 1 (5%) 1 (5%) | 8 6 (75%) 2 (25%) 0 (0%) 0 (0%) 0 (0%) 0 (0%) | 11 6 (55%) 3 (27%) 2 (18%) 0 (0%) 0 (0%) 0 (0%) |
TGA | Total Type 1A Type 3A | 2 1 (50%) 1 (50%) | 0 0 (0%) 0 (0%) | 0 0 (0%) 0 (0%) | |
DORV | Total Type 1A Type 1B Type 2A | 6 4 (66%) 1 (17%) 1 (17%) | 1 1 (100%) 0 (0%) 0 (0%) | 2 0 (0%) 1 (50%) 1 (50%) | |
Hypoplastic LV | Total Type 1A Type 1B Type 2A Type 2B Type 3A Type 3B | 40 24 (60%) 7 (17%) 3 (7.5%) 2 (5%) 3 (7.5%) 1 (3%) | 6 6 (100%) 0 (0%) 0 (0%) 0 (0%) 0 (0%) 0 (0%) | 14 8 (57%) 3 (22%) 1 (7%) 1 (7%) 1 (7%) 0 (0%) | |
Aortic arch hypoplasia | Total Type 1A Type 1B Type 2A Type 3A | 13 7 (54%) 2 (15%) 3 (23%) 1 (8%) | 6 5 (83%) 0 (0%) 0 (0%) 1 (17%) | 8 5 (63%) 1 (12%) 2 (25%) 0 (0%) | |
Aortic coarctation | Total Type 1A Type 1B Type 2A Type 3A | 33 21 (64%) 8 (24%) 1 (3%) 3 (9%) | 4 4 (100%) 0 (0%) 0 (0%) 0 (0%) | 8 2 (25%) 4 (50%) 1 (12.5%) 1 (12.5%) |
*The number of observed cases that could be assessed for this particular abnormality.
ASD, atrial septal defect; AV valve, atrioventricular valve; AVSD, atrioventricular septal defect; BAV, bicuspid aortic valve; DORV, double outlet right ventricle; LCA, left coronary artery; LV,left ventricular; MV, mitral valve; PLSCV, persistent left superior caval vein; RCA, right coronary artery; TGA, transposition of the great arteries; TV, tricuspid valve; VSD, ventricular septal defect.