Table 2

BAV morphology and height of coronaries in different anomalies

BAV morphologyn (%)RCA above STLCA above ST
Inflow and septal defectsPLSCVTotal
Type 1A
Type 1B
Type 2A
Type 2B
Type 3A
Type 3B
15
6 (40%)
2 (13%)
3 (20%
1 (7%)
1 (7%)
2 (13%)
3
3 (100%)
0 (0%)
0 (0%)
0 (0%)
0 (0%)
0 (0%)
4
1 (25%)
0 (0%)
1 (25%)
0 (0%)
1 (25%)
1 (25%)
Muscular VSDTotal
Type 1A
Type 1B
Type 2A
Type 3A
Type 3B
20
12 (60%)
5 (25%)
0 (0%)
2 (10%)
1 (5%)
3
1 (33%)
1 (33%)
0 (0%)
1 (33%)
0 (0%)
8
5 (62%)
2 (25%)
0 (0%)
1 (13%)
0 (0%)
ASDTotal
Type 1A
Type 1B
Type 2A
Type 3A
11
5 (46%)
3 (27%)
2 (18%)
1 (9%)
2
2 (100%)
0 (0%)
0 (0%)
0 (0%)
5
2 (40%)
2 (40%)
0 (0%)
1 (20%)
AVSDTotal
Type 1A
Type 2A
Type 2B
4
2 (50%)
1 (25%)
1 (25%)
1
1 (100%)
0 (0%)
0 (0%)
2
0 (0%)
1 (50%)
1 (50%)
AV valve anomalies
TV dysplasia
TV hypoplasia
TV absent
Total
Type 1A
Type 1B
Type 2A
11
5 (46%)
3 (27%)
3 (27%)
2
1 (50%)
1 (50%)
0 (0%)
3
1 (33%)
1 (33%)
1 (33%)
Total
Type 1A
Type 1B
Type 2A
3
1 (33%)
1 (33%)
1 (33%)
1
1 (100%)
0 (0%)
0 (0%)
1
1 (100%)
0 (0%)
0 (0%)
Total
Type 1A
1
1 (100%)
0
0 (0%)
0
0 (0%)
MV hypoplasia
MV dysplasia
MV atresia
Total
Type 1A
Type 1B
Type 2A
Type 2B
Type 3A
24
12 (50%)
6 (25%)
2 (8%)
1 (4%)
3 (13%)
4
3 (75%)
0 (0%)
1 (25%)
0 (0%)
0 (0%)
8
4 (50%)
2 (25%)
0 (0%)
1 (12.5%)
1 (12.5%)
Total
Type 1A
Type 2B
5
4 (80%)
1 (20%)
0
0 (0%)
0 (0%)
0
0 (0%)
0 (0%)
Total
Type 1A
1
1 (100%)
0
0 (0%)
0
0 (0%)
Outflow defects and LV hypoplasiaPerimembranous VSDTotal
Type 1A
Type 1B
Type 2A
Type 2B
Type 3A
Type 3B
22
10 (45%)
4 (18%)
5 (22%)
1 (5%)
1 (5%)
1 (5%)
8
6 (75%)
2 (25%)
0 (0%)
0 (0%)
0 (0%)
0 (0%)
11
6 (55%)
3 (27%)
2 (18%)
0 (0%)
0 (0%)
0 (0%)
TGATotal
Type 1A
Type 3A
2
1 (50%)
1 (50%)
0
0 (0%)
0 (0%)
0
0 (0%)
0 (0%)
DORVTotal
Type 1A
Type 1B
Type 2A
6
4 (66%)
1 (17%)
1 (17%)
1
1 (100%)
0 (0%)
0 (0%)
2
0 (0%)
1 (50%)
1 (50%)
Hypoplastic LVTotal
Type 1A
Type 1B
Type 2A
Type 2B
Type 3A
Type 3B
40
24 (60%)
7 (17%)
3 (7.5%)
2 (5%)
3 (7.5%)
1 (3%)
6
6 (100%)
0 (0%)
0 (0%)
0 (0%)
0 (0%)
0 (0%)
14
8 (57%)
3 (22%)
1 (7%)
1 (7%)
1 (7%)
0 (0%)
Aortic arch hypoplasiaTotal
Type 1A
Type 1B
Type 2A
Type 3A
13
7 (54%)
2 (15%)
3 (23%)
1 (8%)
6
5 (83%)
0 (0%)
0 (0%)
1 (17%)
8
5 (63%)
1 (12%)
2 (25%)
0 (0%)
Aortic coarctationTotal
Type 1A
Type 1B
Type 2A
Type 3A
33
21 (64%)
8 (24%)
1 (3%)
3 (9%)
4
4 (100%)
0 (0%)
0 (0%)
0 (0%)
8
2 (25%)
4 (50%)
1 (12.5%)
1 (12.5%)
  • *The number of observed cases that could be assessed for this particular abnormality.

  • ASD, atrial septal defect; AV valve, atrioventricular valve; AVSD, atrioventricular septal defect; BAV, bicuspid aortic valve; DORV, double outlet right ventricle; LCA, left coronary artery; LV,left ventricular; MV, mitral valve; PLSCV, persistent left superior caval vein; RCA, right coronary artery; TGA, transposition of the great arteries; TV, tricuspid valve; VSD, ventricular septal defect.