Variable | Data available, N | Median(IQR) | Minimum/maximum |
Age in years at diagnosis | 72 | 14.5 (10–23) | (1-38) |
Age in years at pregnancy | 111 | 29 (24–33) | (15-42) |
Height (cm) | 104 | 178 (173–183) | (166-190) |
Weight (kg) | 102 | 70.0 (63–86) | (48-126) |
Body mass index | 105 | 22 (20–26.5) | (17-40) |
Data available, N | Number | % | |
Functional status | 114 | ||
NYHA class 1 | 111 | 97.3 | |
NYHA class 2 | 3 | 2.7 | |
NYHA class 3 and 4 | 0 | ||
Genotype positive | 116 | 76 | 65.5 |
Family history of MFS | 115 | 66 | 57.4 |
Family history of dissection | 114 | 40 | 35.0 |
Previous ascending aorta replacement | 114 | 14 | 12.3 |
AoR prior to pregnancy <40 mm (echo) | 56 | 80.0 | |
AoR prior to pregnancy 40–44.9 mm (echo) 70 | 70 | 11 | 15.7 |
AoR prior to pregnancy ≥45 mm (echo) | 70 | 3 | 4.3 |
AoR, aortic root; MFS, Marfan syndrome; NYHA, New York Heart Association.