Table 1

Demographic data and patient characteristics

All patientsHLTxLTx
All63 (100)57 (90.5)6 (9.5)
Sex (male)26 (41.3)24 (42.1)2 (33.3)
Cardiac diagnosis5 (7.9)3 (5.3)2 (33.3)
 Simple pre-tricuspid34 (54.0)31 (54.4)3 (50.0)
 Complex24 (38.1)23 (40.3)1 (16.7)
Down syndrome000
Age at ES diagnosis (years)16.0 (8.3–26.5)16.0 (9.0–24.3)19.5 (4.0–33.8)
Previous cardiac surgery10 (15.9)9 (15.8)1 (16.7)
Pre-transplantation evaluation
 Right heart catheterisation
  PVR, WU18.5 (12.3–28.7)18.0 (12.2–29.0)20.0 (13.1–20.0)
  PAPs/PAPd/PAPm111.5/54.0/81.5115.0/58.0/84.5100.0/48.0/64.5
 SAT at rest (%)82.0 (75.0–88.0)81.0 (74.0–85.0)88.5 (76.5–91.2)
 6MWD (m)290 (170–340)320 (175–345)164 (34.3–233.8)
  SAT during exercise (%)64.0 (56.0–70.0)63.0 (53.5–70.5)68.0 (67.0–68.0)
 Blood tests
  Creatinine (μmol/L)81.5 (72.0–95.0)83.5 (73.5–95.8)74.5 (59.3–91.3)
  Haematocrit0.60 (0.50–0.65)0.60 (0.51–0.65)0.42 (0.39–0.63)
  Haemoglobin (g/L)174 (150–201)174 (150–203)156 (140–211)
  • Values are presented as n (%) or as median (IQR).

  • HLTx, heart–lung transplantation; LTx, lung transplantation; 6MWD, 6 min walking distance; PAPd, diastolic pulmonary artery pressure; PAPm, mean pulmonary artery pressure; PAPs, systolic pulmonary artery pressure; PVR, pulmonary vascular resistance; SAT, oxygen saturation; WU, Wood units.