Table 2

Anatomic causes of heart failure in congenital heart disease

Anatomic challengesLesionsPotential surgeries or interventionsPotential residual abnormalitiesPotential sequelaeEvaluation
Systemic right ventricleccTGA
  • Tricuspid valve repair or replacement

  • VSD closure

Tricuspid regurgitationHeart block
  • TTE

  • CT

  • MRI

  • Cardiac catheterisation

D-TGAAtrial switch procedure (Mustard or Senning)
  • Baffle stenosis or leak

  • Tricuspid regurgitation

Sinus node dysfunction
OtherD-TGAArterial switch operation
  • Coronary ostial stenosis

  • Aortic dilation

  • Aortic regurgitation

Single ventricle anatomy (ie, double inlet left ventricle, tricuspid atresia)Fontan palliation
  • Outflow tract obstruction

  • Atrioventricular valve regurgitation

  • Atrial arrhythmias

  • Chronic hepatic congestion

  • Protein-losing enteropathy

  • Plastic bronchitis

  • TTE

  • CT

  • MRI

  • Cardiac catheterisation

  • Liver evaluation

  • ccTGA, congenitally corrected transposition of the great arteries; D-TGA, D-transposition of the great arteries; ; TTE, transthoracic echocardiogram; VSD, ventricular septal defect.