Revised Ghent criteria systemic score7
| Systemic feature | Points |
| Wrist and thumb sign | 3 |
| Wrist or thumb sign | 1 |
| Pectus carinatum | 2 |
| Pectus excavatum or chest asymmetry | 1 |
| Pneumothorax | 2 |
| Dural ectasia | 2 |
| Protrusio acetabuli | 2 |
| Reduced US/LS and increased arm/height and no severe scoliosis | 1 |
| Scoliosis or thoracolumbar kyphosis | 1 |
| Reduced elbow extension | 1 |
| Three of five features: dolichocephaly, enophthalmos, downslanting palpebral fissures, malar hypoplasia and retrognathia | 1 |
| Skin striae | 1 |
| Myopia >3 dioptres | 1 |
| Mitral valve prolapse | 1 |
Maximum score of 20 points; score >7 indicates systemic involvement.
Marfan systemic score features may be visualised at www.Marfan.org.
US/LS, upper segment/lower segment ratio.