Table 1

Causes of sudden cardiac death

Vascular diseaseMyocardial infarction 2° to atherosclerotic disease (premature atherosclerosis in familial hypercholesterolaemia)
Ischaemia/scar-related ventricular arrhythmia
Anomalous coronary arteries
Coronary artery vasospasm
Aortic rupture (Marfan's syndrome predominant genetic pathology)
CardiomyopathyDilated cardiomyopathy (including Lamin cardiomyopathies)
Hypertrophic cardiomyopathy
Arrhythmogenic right ventricular cardiomyopathy
Myotonic dystrophy
Inflammatory disordersMyocarditis
Amyloidosis
Sarcoidosis
Valve disordersAortic stenosis
Mitral valve prolapse (rare malignant form)
Arrhythmia syndromesBrugada syndrome
Catecholaminergic polymorphic VT
Long QT syndrome
Short QT syndrome
Wolff Parkinson's White syndrome
Other early repolarisation (J wave) syndromes
TraumaCommotio cordis