Table 2

Pulmonary artery anomalies and outcome

PatientCPA confluenceNumber of MAPCAArborisation anomaliesOutcome
1Yes2RPABiventricular repair probably possible
2Yes5BilateralDefinite palliation
3Yes2NoBiventricular repair probably possible
4Yes4BilateralDefinite palliation
5Yes4BilateralUnifocalisation impossible due to intrapulmonary stenoses
6No2BilateralBiventricular repair probably possible, requiring successful unifocalisation
7Yes2BilateralUnifocalisation impossible due to intrapulmonary stenoses
8Yes4BilateralDefinite palliation
9No2LPABiventricular repair probably possible requiring successful unifocalisation
10Yes4BilateralDefinite palliation
11Yes1 NoBiventricular repair
12Yes3RPADefinite palliation, PH of LPA
13Yes2NoBiventricular repair probably possible
14Yes3NoBiventricular repair
15Yes4NoBiventricular repair
16Yes5LPADefinite palliation due to persisting hypoplasia of CPA
17Yes3NoBiventricular repair
18No4BilateralBiventricular repair performed following successful unifocalisation
19Yes4NoBiventricular repair probably possible
20Yes2NoBiventricular repair
21Yes2NoBiventricular repair
  • CPA, central pulmonary arteries; LPA, left pulmonary artery; MAPCA, major aortopulmonary collateral arteries; PH, pulmonary hypertension; RPA, right pulmonary artery.